From: Management of late onset urea cycle disorders—a remaining challenge for the intensivist?
Treatment | Patients (n) | % |
---|---|---|
Low protein oral nutrition | 28 | 73 |
Benzoate | 27 | 46 |
L-Arginine | 21 | 50 |
Dialysis | 14 | 34 |
Phenylbutyrate | 10 | 19 |
L-Carnitine | 7 | 27 |
Citruline | 4 | 15 |
Low protein parenteral nutrition | 7 | 15 |
Hepatic transplantation | 4 | 7 |